Factor XI deficiency and orthognathic surgery: a case report on anesthesia management
이수언, 최윤지, 지성인, 김현정, 서광석,
소속 상세정보
이수언 ( Lee Soo-Eon ) - Seoul National University Dental Hospital Department of Dental Anesthesiology
최윤지 ( Choi Yoon-Ji ) - Seoul National University Dental Hospital Department of Dental Anesthesiology
지성인 ( Chi Seong-In ) - Seoul National University Dental Hospital Department of Dental Anesthesiology
김현정 ( Kim Hyun-Jeong ) - Seoul National University Dental Hospital Department of Dental Anesthesiology
서광석 ( Seo Kwang-Suk ) - Seoul National University Dental Hospital Department of Dental Anesthesiology
KMID : 0980320150150010025
Abstract
Factor XI deficiency (Hemophilia C) is a very rare autosomal recessive bleeding disorder. Patients with factor XI deficiency do not typically show any spontaneous bleeding or specific symptoms. Sometimes those who have this disorder are identified during special situations such as trauma or surgery. Orthognathic surgery is particularly associated with a high bleeding risk. Therefore, great care must be taken when treating patients with bleeding disorders such as factor XI deficiency. There are a few reports that address the management of patients with bleeding disorders during orthognathic surgery. The current report describes a patient with factor XI deficiency who underwent Le Fort I osteotomy together with bilateral sagittal split osteotomy. The patient’s condition was assessed using both rotation thromboelastometry (ROTEMTM) and noninvasive measurements of total hemoglobin (SpHb) using Masimo Radical 7 (Masimo Co. CA, USA).
키워드
Continuous noninvasive hemoglobin monitoring; Factor XI deficiency; Orthognathic surgery; Rotation thromboelastometry
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